Adamantinomatous craniopharyngioma.

Abstract

Introduction: The purpose of this article is to describe the main clinical manifestations, diagnostic method and treatment of choice of a rare primary intracranial neoplasia of epithelial origin, benign with its adamantinomatous variant typical of pediatric age that is diagnosed more frequently in age ranges from 5 to 14 years according to the international scientific literature review. Clinical case: A case is reported in which the patient is not within the age peaks in which the diagnosis of adamantinomatous craniopharyngioma is most frequently made; it is a 17-year-old female patient with headache and dysmenorrhea of 6 months of age. Evolution accompanied by bitemporal hemianopia that underwent open cranial surgery through the right pterional approach with subtotal resection of the lesion, and a peritoneal ventricular shunt was placed due to obstructive tetraventricular hydrocephalus that was developed one year after surgery. Conclusions: The symptoms coincide with the symptoms described and attributable to compression and extension towards adjacent structures, its presentation was slow in evolution, the image was characteristic of this pediatric histological variant. Despite being a benign histology entity, it is aggressive due to its invasion of deep and autonomic structures, causing an uncertain natural history and with a high probability of comorbidities that may be greater with aggressive surgical treatments.